{"id":7329,"date":"2017-08-04T20:49:22","date_gmt":"2017-08-04T20:49:22","guid":{"rendered":"http:\/\/doctorexpres.ro\/?p=7329"},"modified":"2017-08-05T09:50:53","modified_gmt":"2017-08-05T09:50:53","slug":"mormonii-poligami-o-comunitate-de-mutanti","status":"publish","type":"post","link":"https:\/\/doctorexpres.ro\/index.php\/2017\/08\/04\/mormonii-poligami-o-comunitate-de-mutanti\/","title":{"rendered":"Mormonii poligami, o comunitate de mutan\u0163i"},"content":{"rendered":"<p style=\"text-align: justify;\" align=\"JUSTIFY\">Copiii mormonilor din Arizona s\u00eent genetic degenera\u0163i. Cauza? Poligamia din comunitate.<!--more--><\/p>\n<p style=\"text-align: justify;\" align=\"JUSTIFY\">\u00cen anii 90, Th\u00e9odore Taby, un medic american specializat \u00een bolile rare ale copil\u0103riei, s-a confruntat cu cazul unui copil cu tr\u0103s\u0103turi fizice neobi\u0219nuite: frunte proeminent\u0103, <a href=\"http:\/\/doctorexpres.ro\/index.php\/2017\/02\/02\/6-metode-de-scos-apa-din-urechi\/\" target=\"_blank\">urechi<\/a> c\u0103zute, ochi foarte dep\u0103rta\u0163i, maxilar mic \u0219i incapacitatea de a se a\u015feza sau de <a href=\"http:\/\/doctorexpres.ro\/index.php\/2016\/06\/17\/mersul-pe-jos-beneficii-incredibile-pentru-inima\/\" target=\"_blank\">a merge pe jos<\/a>. Potrivit specialistului, copilul suferea de acidurie fumaric\u0103, o boal\u0103 extrem de rar\u0103. Doar 13 cazuri au fost identificate la momentul respectiv.<\/p>\n<p style=\"text-align: justify;\" align=\"JUSTIFY\">Consecin\u021bele pot fi grave: \u201ea<em>nomalii structurale \u0219i un sindrom cu convulsii \u015fi \u00eent\u00eerzieri \u00een dezvoltare<\/em>\u201c, conform neurologului Vinodh Narayanan. Boala se dezvolt\u0103 dac\u0103 individul mo\u0219tene\u0219te gena defect\u0103 de la oricare dintre <a href=\"http:\/\/doctorexpres.ro\/index.php\/2017\/04\/26\/abilitatile-cognitive-difera-de-la-parinti-la-copii-si-de-la-o-cultura-la-alta\/\" target=\"_blank\">p\u0103rin\u0163i<\/a>. \u201e<em>C\u00eend oamenii se c\u0103s\u0103toresc \u00eentre ei \u00een aceea\u0219i comunitate, cresc \u0219ansele de a exista doi oameni care poart\u0103 exact aceeasi<a href=\"http:\/\/doctorexpres.ro\/index.php\/2016\/08\/08\/dopajul-viitorului-manipularea-genetica\/\" target=\"_blank\"> muta\u0163ie genetic\u0103<\/a><\/em>\u201c, spune neurologul.<\/p>\n<p style=\"text-align: justify;\" align=\"JUSTIFY\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-7346 alignleft\" src=\"http:\/\/doctorexpres.ro\/wp-content\/uploads\/2017\/08\/JulieHall4-350x525-200x300.jpg\" alt=\"JulieHall4-350x525\" width=\"200\" height=\"300\" srcset=\"https:\/\/doctorexpres.ro\/wp-content\/uploads\/2017\/08\/JulieHall4-350x525-200x300.jpg 200w, https:\/\/doctorexpres.ro\/wp-content\/uploads\/2017\/08\/JulieHall4-350x525.jpg 350w\" sizes=\"auto, (max-width: 200px) 100vw, 200px\" \/>Opt cazuri noi au fost detectate recent \u00een ora\u0219ul Short Creek, Arizona, unde tr\u0103iesc mormoni poligami, o practic\u0103 interzis\u0103 de Biserica Mormon\u0103 oficial\u0103 \u00een 1890.<\/p>\n<p style=\"text-align: justify;\" align=\"JUSTIFY\">Via\u021ba retras\u0103 \u0219i<a href=\"http:\/\/doctorexpres.ro\/index.php\/2016\/07\/28\/de-ce-in-comunitatile-amish-nu-exista-cancer-diabet-si-autism\/\" target=\"_blank\"> poligamia<\/a> favorizeaz\u0103 consangvinitatea, aflat\u0103 la originea diverselor handicapuri \u00een r\u00eendul mormonilor. \u201e<em>S\u00eent complet handicapa\u0163i fizic \u015fi mintal<\/em>\u201c, spune Faith Bistline, un fost membru. Cinci dintre verii s\u0103i s\u00eent afecta\u0163i de boal\u0103 \u015fi trebuie s\u0103 se alimenteze cu sond\u0103. Cel mai v\u00eerstnic a \u00eenv\u0103\u021bat s\u0103 mearg\u0103 la v\u00eersta de 2 ani, dar nu a mai putut continua din cauza crizelor convulsive severe. La 30 de ani, nu este capabil nici s\u0103 se t\u00eerasc\u0103.<\/p>\n<p style=\"text-align: justify;\" align=\"JUSTIFY\">Prin c\u0103s\u0103torii \u00eentre rude, <a href=\"http:\/\/doctorexpres.ro\/index.php\/2016\/10\/21\/regiunea-unde-traiesc-cei-mai-multi-giganti\/\" target=\"_blank\">muta\u0163ia genetic\u0103<\/a> se perpetueaz\u0103 exponen\u0163ial \u00een<a href=\"http:\/\/doctorexpres.ro\/index.php\/2017\/05\/30\/de-ce-serpasii-aproape-nu-au-nevoie-de-oxigen\/\" target=\"_blank\"> comunitate<\/a>. Chiar \u0219i cu o singur\u0103 so\u021bie \u0219i trei copii, un b\u0103rbat poate avea 243 descenden\u021bi, dup\u0103 doar cinci<a href=\"http:\/\/doctorexpres.ro\/index.php\/2016\/07\/11\/efectele-fast-food-se-intind-pe-trei-generatii\/\" target=\"_blank\"> genera\u021bii<\/a>. Dac\u0103 fiecare genera\u021bie include trei neveste \u0219i 30 de<a href=\"http:\/\/doctorexpres.ro\/index.php\/2017\/07\/26\/copiii-de-la-tara-sint-mai-feriti-de-boli-inflamatorii-intestinale\/\" target=\"_blank\"> copii <\/a>(conform mediei statistice), un mormon poate &#8211; teoretic &#8211; s\u0103 inunde o comunitate cu peste 24 de milioane de descenden\u021bi \u00een spa\u021biul a cinci genera\u021bii sau pu\u021bin peste 100 de ani. Brigham Young, \u00een 1982, avea cel pu\u021bin 5.000 de descenden\u021bi direc\u021bi.\u00a0Ast\u0103zi, num\u0103rul de persoane din Short Creek care au gena fumarazei este considerat a fi de ordinul miilor.<\/p>\n<p style=\"text-align: justify;\" align=\"JUSTIFY\">Conform <a href=\"http:\/\/www.bbc.com\/future\/story\/20170726-the-polygamous-town-facing-genetic-disaster\" target=\"_blank\">BBC<\/a>, \u00een Short Creek, doar dou\u0103 nume de familie domin\u0103 <a href=\"http:\/\/doctorexpres.ro\/index.php\/2017\/03\/09\/a-fost-descoperita-o-populatie-cu-toleranta-la-arsenic\/\" target=\"_blank\">comunitatea<\/a> local\u0103: Jessop \u0219i Barlow. Potrivit istoricului local Benjamin Bistline, care a f\u0103cut declara\u0163ii pentru Reuters \u00een 2007, 75 p\u00een\u0103 la 80% dintre persoanele din Short Creek s\u00eent rude de s\u00eenge ale patriarhilor fondatori ai comunit\u0103\u021bii, Joseph Jessop \u0219i John Barlow.<\/p>\n<p style=\"text-align: justify;\" align=\"JUSTIFY\">Ast\u0103zi, poligamia este mai r\u0103sp\u00eendit\u0103 \u00een Africa. \u00cen martie 2014, Parlamentul din Kenya a adoptat un proiect de lege care permite b\u0103rba\u021bilor s\u0103 se c\u0103s\u0103toreasc\u0103 cu mai multe so\u021bii, \u00een timp ce \u00een multe \u021b\u0103ri din Africa de Vest, poligamia e practicat\u0103 de mii de ani.<\/p>\n<p style=\"text-align: justify;\" align=\"JUSTIFY\">Sursa: <a href=\"http:\/\/www.20minutes.fr\/societe\/2112683-20170802-etats-unis-mormons-polygames-frappes-maladie-genetique-rare\" target=\"_blank\">20minutes.fr<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Copiii mormonilor din Arizona s\u00eent genetic degenera\u0163i. Cauza? Poligamia din comunitate.<\/p>\n","protected":false},"author":4,"featured_media":7345,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[98,99],"tags":[10745,10753,10746,10750,10755,10756,10754,5396,10749,8068,10751,10752,10748,10747],"class_list":["post-7329","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-controverse","category-sanatatea-familiei","tag-acidurie-fumarica","tag-anomalii-structurale","tag-boli-foarte-rare","tag-consangvinitate","tag-fumaraza","tag-handicap","tag-intarzieri-in-dezvoltare","tag-mormoni","tag-mormoni-poligami","tag-mutatie-genetica","tag-poligamie","tag-short-creek","tag-theodore-taby","tag-vinodh-narayanan"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.7 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Mormonii poligami, o comunitate de mutan\u0163i - Doctor Expres<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/doctorexpres.ro\/index.php\/2017\/08\/04\/mormonii-poligami-o-comunitate-de-mutanti\/\" \/>\n<meta property=\"og:locale\" content=\"ro_RO\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Mormonii poligami, o comunitate de mutan\u0163i - Doctor Expres\" \/>\n<meta property=\"og:description\" content=\"Copiii mormonilor din Arizona s\u00eent genetic degenera\u0163i. 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